Cart
sales@molnova.com
2-Hydroxy-3-methylbutyric acid
CAS No. 4026-18-0
2-Hydroxy-3-methylbutyric acid( 2-Hydroxy-3-methylbutanoic acid | (±)-2-Hydroxyisopentanoic Acid | 2-Hydroxyisovaleric Acid )
Catalog No. M19995 CAS No. 4026-18-0
2-Hydroxy-3-methylbutyric acid (2-hydroxyisovaleric acid) is a metabolite found in the urine of patients with phenylketonuria methylmalonic acidemia propionic acidemia 3-ketothiolase deficiency isovaleric acidemia 3-methylcrotonylglycemia 3-hydroxy-3-methylglutaric acidemia multiple carboxylase deficiency glutaric aciduria ornithine transcarbamylase deficiency glyceroluria tyrosinemia type I galactosemia and maple syrup urine disease.
Purity : >98% (HPLC)
COA
Datasheet
HNMR
HPLC
MSDS
Handing Instructions
| Size | Price / USD | Stock | Quantity |
| 1 mL x 10 mM in DMSO | 28 | In Stock |
|
| 100MG | 29 | In Stock |
|
| 200MG | Get Quote | In Stock |
|
| 500MG | 65 | In Stock |
|
| 1G | 91 | In Stock |
|
Biological Information
-
Product Name2-Hydroxy-3-methylbutyric acid
-
NoteResearch use only, not for human use.
-
Brief Description2-Hydroxy-3-methylbutyric acid (2-hydroxyisovaleric acid) is a metabolite found in the urine of patients with phenylketonuria methylmalonic acidemia propionic acidemia 3-ketothiolase deficiency isovaleric acidemia 3-methylcrotonylglycemia 3-hydroxy-3-methylglutaric acidemia multiple carboxylase deficiency glutaric aciduria ornithine transcarbamylase deficiency glyceroluria tyrosinemia type I galactosemia and maple syrup urine disease.
-
Description2-Hydroxy-3-methylbutyric acid (2-hydroxyisovaleric acid) is a metabolite found in the urine of patients with phenylketonuria methylmalonic acidemia propionic acidemia 3-ketothiolase deficiency isovaleric acidemia 3-methylcrotonylglycemia 3-hydroxy-3-methylglutaric acidemia multiple carboxylase deficiency glutaric aciduria ornithine transcarbamylase deficiency glyceroluria tyrosinemia type I galactosemia and maple syrup urine disease.
-
In Vitro——
-
In Vivo——
-
Synonyms2-Hydroxy-3-methylbutanoic acid | (±)-2-Hydroxyisopentanoic Acid | 2-Hydroxyisovaleric Acid
-
PathwayOthers
-
TargetOther Targets
-
RecptorOthers
-
Research Area——
-
Indication——
Chemical Information
-
CAS Number4026-18-0
-
Formula Weight118.13
-
Molecular FormulaC5H10O3
-
Purity>98% (HPLC)
-
SolubilityDMSO:194.7 mM
-
SMILESCC(C)C(O)C(O)=O
-
Chemical Name——
Shipping & Storage Information
-
Storage(-20℃)
-
ShippingWith Ice Pack
-
Stability≥ 2 years
Reference
-
Atrial Natriuretic F...
Atrial natriuretic peptide (3-28) (human) (ANP (3-28) (human)) is a peptide hormone that is synthesized and secreted by the atrial myocardium. Atrial natriuretic peptide (3-28) (human) is involved in the regulation of blood pressure, fluid balance, and electrolyte homeostasis.
-
FITC-LC-Myelin Basic...
FITC-LC-Myelin Basic Protein Peptide Substrate
-
ELA-32 (human)
Potent, high affinity apelin receptor agonist (IC50 = 0.27 nM; Kd = 0.51 nM). Exhibits no binding GPR15 and GPR25. Activates the PI3K/AKT pathway and promotes self-renewal of hESCs via cell-cycle progression and protein translation. Also potentiates the TGFβ pathway, priming hESCs toward the endoderm lineage. Stimulates angiogenesis in HUVEC cells. Relaxes mouse aortic vessels. Functions as an anorexigenic hormone through activation of the AVP and CRH neurons in the PVN.
