L-allo-Isoleucine ( (3R)-LS-Isoleucine;L(+)-Alloisoleucine )

Catalog No. M20000 CAS No. 1509-34-8

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Product Name

L-allo-Isoleucine
Note

Research use only not for human use.
Brief Description

L-alloisoleucine is a branched chain amino acid and is a stereoisomer of L-isoleucine. It is a common constituent of human plasma (albeit at low levels). L-alloisoleucine is produced as a byproduct of isoleucine transamination. Plasma L-alloisoleucine which is derived from L-isoleucine in vivo can be used for the diagnosis of maple syrup urine disease (MSUD) a genetic disorder.
Description

L-alloisoleucine is a branched chain amino acid and is a stereoisomer of L-isoleucine. It is a common constituent of human plasma (albeit at low levels). L-alloisoleucine is produced as a byproduct of isoleucine transamination. Plasma L-alloisoleucine which is derived from L-isoleucine in vivo can be used for the diagnosis of maple syrup urine disease (MSUD) a genetic disorder. Indeed plasma L-alloisoleucine levels above 5 μmol/L is the most specific and most sensitive diagnostic marker for all forms of MSUD.
Synonyms

(3R)-LS-Isoleucine;L(+)-Alloisoleucine
Pathway

Others
Target

Other Targets
Recptor

Others
Research Area

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Indication

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1.Schadewaldt P et al. Significance of L-alloisoleucine in plasma for diagnosis of maple syrup urine disease. Clin Chem. 1999 Oct;45(10):1734-40.

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