Glutarylcarnitine( —— )

Catalog No. M33601 CAS No. 102636-82-8

COA

Datasheet

HNMR

HPLC

MSDS

Handing Instructions

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Product Name

Glutarylcarnitine
Note

Research use only, not for human use.
Brief Description

Glutarylcarnitine (O-glutaroyl-L-carnitine) is a diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.
Description

Glutarylcarnitine is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.
In Vitro

Malonylcarnitine and Glutarylcarnitine are important diagnostic metabolites in the screening of dried blood spots by tandem mass spectrometry.The urinary excretion of glutarylcarnitine is a specific biochemical marker of glutaric acidemia type I (GA-1). The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I.
In Vivo

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Synonyms

——
Pathway

Proteasome/Ubiquitin
Target

Endogenous Metabolite
Recptor

Endogenous Metabolite
Research Area

——
Indication

——

CAS Number

102636-82-8
Formula Weight

275.3
Molecular Formula

C12H21NO6
Purity

>98% (HPLC)
Solubility

In Vitro:?Ethanol : 100 mg/mL (363.24 mM; Ultrasonic)DMSO : 2 mg/mL (7.26 mM; Ultrasonic (<60°C)
SMILES

[C@H](OC(CCCC(O)=O)=O)(C[N+](C)(C)C)CC([O-])=O
Chemical Name

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1. Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27(6):789-90.?

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